[CITATION][C] A new familial immunodeficiency disorder characterized by severe neutropenia, a defective marrow release mechanism, and hypogammaglobulinemia

M Wetzler, M Talpaz, ES Kleinerman, A King… - The American journal of …, 1990 - Elsevier
MEIR WETZLER, MD, MOSHE TALPAZ, MD, EUGENIE S. KLEINERMAN, MD, ALICE KING,
MD, YANG O. HUH, MD, JORDAN U. GUTTERMAN, MD, RAZELLE KURZROCK, MD,
Houston, Texas l mmunocompromise may result from a defect in. any of the effectors of the
immune system, including T and B lymphocytes, phagocytic cells, and complement proteins
[1-5]. Genetically determined immunodeficiency syndromes are considered rare. However,
their importance lies not only in their significance to the individuals affected by them, but also …